| Sklerodermie |
| |
|
| |
Syn: Engl: systemic
sclerosis |
| |
ICD-10: M34 (SystemSklerose)
M34.0 Progressive Syst.Sklerose M34.1 (Crest-Syndrom), L94.0
(Sclerodermia circumscripta/Morphaea) P83.8 Sklerodermie
beim NG |
| |
HER / Neur1 / DERM1 |
| |
|
| |
|
| |
|
| |
|
| |
|
| |
|
|
|
Systemsklerose |
|
 |
|
|
| |
|
Progressive
Systemsklerose |
|
 |
|
|
| |
|
CREST-Syndrom |
|
 |
|
Calcinosis,
Raynaud phenomena, Esophageal
hypomotility, Sclerodactyly, Teleangiectasia;
limitierte Unterform der
Systemsklerose |
| |
|
zirkumskripte
Sklerodermie |
|
 |
|
auf
Haut, Subcutis, gelegentlich Muskulatur und
Knochen beschränkt |
|
| |
|
| |
|
|
|
zu
den Kollagenosen zählende
AutoimmunKH |
|
|
|
|
| |
|
mit
Bindegewebsverhärtung der Haut alleine oder der
Haut und innerer Organe (va GIT, Lunge, Herz,
Nieren) |
|
|
|
|
|
| |
|
 |
|
| |
|
 |
|
| |
|
| |
|
| |
|
 |
|
| |
|
 |
| -
|
- |
- |
- |
- |
- |
- |
| - |
- |
-- |
- |
- |
- |
- |
| - |
- |
- |
- |
- |
- |
- |
| - |
- |
- |
- |
- |
- |
- |
|
| |
|
 |
|
| |
|
 |
| andere Kollagenosen |
|
|
|
SLE |
|
 |
|
Leitsy:
Lupuserythem |
|
|
|
Sklerodermie |
|
 |
|
Leitsy:
derbe Infiltration der Haut |
|
|
|
primäres
Sjögren-Syndrom |
|
 |
|
Leitsy:
Xerostomie, Xerophthalmie |
|
| |
|
| |
|
| |
|
| |
|
 |
|
|
|
ANA,
|
|
|
|
|
| |
|
(progr.)
Systemsklerose |
|
 |
|
Anti-SCL
70 |
|
|
|
CREST-Syndrom |
|
 |
|
Anti-Zentromer-Ak |
| |
|
|
|
|
|
|
|
|
|
|
|
|
|
|
| |
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
| |
|
| |
|
| |
|
 |
|
| |
|
| |
|
| |
|
 |
|
| |
|
| |
|
| |
|
| |
|
| |
|
 |
|
| |
|
| |
|
| |
|
| |
 |
|
|
|
 |
|
wg.
Sclerodermal Renal Crisis4 |
|
| |
|
| |
| x |
| |
|
| |
|
| quelle |
quelle |
| x |
| |
|
| |
|
| quelle |
quelle |
|
| |
|
| |
|
| |
|
 |
Robbins / Curran / Laissue |
| |
| |
|
|
|
Allgemein: |
|
|
| |
|
|
|
|
|
|
|
Makro:
|
|
|
| |
|
|
|
|
|
|
|
Mikro:
|
|
|
| |
|
|
|
|
|
|
|
DD: |
|
|
|
| |
|
 |
|
| |
|
| |
|
| Quellen |
Verlauf |
Links |
| |
|
|
|
|
| begonnen |
|
29.04.11 |
|
- |
| aktualisiert: |
|
- |
|
- |
| |
|
- |
|
- |
| broken Links: |
|
29.04.11 |
|
- |
| Rückmeldungen
via emaille |
| Legende / Farbcode |
| Haftungsausschluss / Disclaimer |
|
|
|
| |
|